The protein encoded by this gene is an enzyme that elongates the prenyl side-chain of coenzyme Q, or ubiquinone, one of the key elements in the respiratory chain. The gene product catalyzes the formation of all trans-polyprenyl pyrophosphates from isopentyl diphosphate in the assembly of polyisoprenoid side chains, the first step in coenzyme Q biosynthesis. The protein may be peripherally associated with the inner mitochondrial membrane, though no transit peptide has been definitively identified to date. Defects in this gene are a cause of coenzyme Q10 deficiency. [provided by RefSeq, Jul 2008]
| SKU | Test Kits | Buffer | Dye Color | Order Now |
|---|---|---|---|---|
| PDSS1-20-RE | 20 (40 μL) | 200 μL |  |
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| PDSS1-20-OR | 20 (40 μL) | 200 μL |  |
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| PDSS1-20-GO | 20 (40 μL) | 200 μL |  |
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| PDSS1-20-GR | 20 (40 μL) | 200 μL |  |
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| PDSS1-20-AQ | 20 (40 μL) | 200 μL |  |
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The protein encoded by this gene is an enzyme that elongates the prenyl side-chain of coenzyme Q, or ubiquinone, one of the key elements in the respiratory chain. The gene product catalyzes the formation of all trans-polyprenyl pyrophosphates from isopentyl diphosphate in the assembly of polyisoprenoid side chains, the first step in coenzyme Q biosynthesis. The protein may be peripherally associated with the inner mitochondrial membrane, though no transit peptide has been definitively identified to date. Defects in this gene are a cause of coenzyme Q10 deficiency. [provided by RefSeq, Jul 2008]
Gene Symbol : PDSS1
Gene Name : Decaprenyl diphosphate synthase subunit 1
Chromosome : CHR 10: 266,970,51-267,467,97
Locus : 10p12.1
Alt. Genes : FEM1B
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